…There are various demyelinating diseases, but they can be broadly divided into (1) those based on lipid metabolism disorders, (2) those due to autoimmunity, (3) those due to viral infection, and (4) those of unknown cause. (1) Demyelinating diseases due to lipid metabolism disorders include the aforementioned hypomyelination, but because myelin is lost over a wide area of the cerebral white matter, they are called leukodystrophy. However, there are also diseases with a confirmed defective enzyme in lipid metabolism, such as metachromatic leukodystrophy (arylsulfatase A deficiency) and Krabbe's disease (galactocerebrosidase deficiency). … *Some of the terminology that mentions "leukodystrophy" is listed below. Source | Heibonsha World Encyclopedia 2nd Edition | Information |
…脱髄疾患には種々のものがあるが,(1)脂質代謝異常に基づくもの,(2)自己免疫によるもの,(3)ウイルス感染によるもの,(4)原因不明のもの,に大別される。(1)脂質代謝異常による脱髄疾患には,前述の髄鞘形成不全というべきものが含まれているが,大脳白質の広い範囲にわたって髄鞘が消失するため,白質ジストロフィーleukodystrophyと呼ばれている。しかし脂質代謝異常の欠損酵素が確定しているものとしては,異染性白質ジストロフィー(アリルスルファターゼA欠損症)や,クラッベ病Krabbe’s disease(ガラクトセレブロシダーゼ欠損症)などがある。… ※「leukodystrophy」について言及している用語解説の一部を掲載しています。 出典|株式会社平凡社世界大百科事典 第2版について | 情報 |
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